Systemic vasculitis complicating infantile autoimmune enteropathy.
نویسندگان
چکیده
An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatment with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapheresis resulted in resolution of the vasculitic process but the child subsequently died after overwhelming septicaemia.
منابع مشابه
A rare cause of protein-losing enteropathy and growth retardation in infancy: infantile systemic hyalinosis.
Infantile systemic hyalinosis is a rare, progressive, fatal condition with a presumably autosomal recessive mode of inheritance. It is characterized by widespread deposition of hyaline material in many tissues. We present a three-month-old girl with hypoproteinemia, growth retardation, and generalized stiff and edematous skin, who was diagnosed as protein-losing enteropathy. A final diagnosis o...
متن کاملCryoglobulinic Vasculitis in Children (Case Report)
Introduction: The systemic vasculitis have varicose etiology that most of them are caused by autoimmune problems. One kind of systemic vas is caused by the plenty amount of cryoglubulin in blood. Case report: A 3 year old boy with cutaneous, joint, and CNS manifestations that is diagnosed with cryoglubolinemic vasculitis. Discussion: Cryoglubolinemic vasculitis with CNS involvement and bleeding...
متن کاملThyroid Involvement in Hepatitis C Virus-Infected Patients with/without Mixed Cryoglobulinemia
Thyroid involvement is a common condition that can be recorded during the natural course of different systemic rheumatic diseases, including the mixed cryoglobulinemia (MC) syndrome or cryoglobulinemic vasculitis. MC is triggered by hepatitis C virus (HCV) chronic infection in the majority of cases; it represents the prototype of autoimmune-lymphoproliferative disorders complicating a significa...
متن کاملSystemic Lupus Erythematosus and the Vasculitides
Systemic lupus erythematosus (SLE) is a multisystem, autoimmune disorder that poses a challenge to the emergency physician with its protean and occasionally dangerous manifestations. Morbidity for SLE patients is typically mediated through organ inflammation and destruction or the consequences of therapeutic immunosuppression. Further complicating lupus is the frequent association with the anti...
متن کاملChronic Diarrhea Unmasking Systemic Lupus Erythematosus
Systemic lupus erythematosus (SLE) is an autoimmune disorder characterized by multisystem inflammation, autoantibody formation, and immune complex deposition in nearly any organ system. Age of presentation is typically around the third decade, more likely in females of African, Hispanic, and Asian origin [1]. The most common initial symptoms include fever, arthralgia, and malar rash. Gastrointe...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Archives of disease in childhood
دوره 72 5 شماره
صفحات -
تاریخ انتشار 1994